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KMID : 0390020110210020131
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Pediatric Allergy and Respiratory Disease
2011 Volume.21 No. 2 p.131 ~ p.136
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A Case of Laryngeal Neurofibroma with Sleep Obstructive Apnea
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Kim Ju-Hyun
Ko Hoon
Seo Ju-Hee
Kim Hyung-Young
Yu Jin-Ho
Hong Soo-Jong
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Abstract
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Most patients with neurofibromas suffer from neurofibromatosis type 1 (von Recklinghausen’s disease), which is characterized by cafe-au-lait spots and cutaneous neurofibromas. Neurofibromas in the laryngeal area are extremely rare. Most patients with a laryngeal neurofibroma present with dyspnea, dysphagia, stridor, or hoarseness, depending on the location and size of the tumor. We present a case of a laryngeal neurofibroma in a boy with neurofibromatosis type 1. A 30-month-old boy with neurofibromatosis presented to our hospital with respiratory difficulty and obstructive sleep apnea. Magnetic resonance imaging demonstrated a round mass over the left carotid space, and its location made surgical resection impossible. Hence, tracheostomy was performed to maintain airway patency. The patient’s symptoms improved after tracheostomy. Long-term follow-up is essential owing to the possibility of recurrence. The patient has thus far shown no obstructive airway symptoms for one year after closure of the tracheostomy.
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KEYWORD
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Neurofibroma, Neurofibromatosis, Larynx, Obstructive airway symptoms
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